CLINICAL STUDY OF SPLENECTOMY AND CHOLECYSTECTOMY FOR HEREDITARY SPHEROCYTOSIS
نویسندگان
چکیده
منابع مشابه
Management of Anesthesia During Splenectomy and Cholecystectomy in a Pregnant Woman With Hereditary Spherocytosis
Hereditary spherocytosis (HS) is a familial hemolytic disorder with intracorpuscular mechanism that characterized by the production of red blood cells with sphere-like shape prone to hemolysis and can lead to hemolytic anemia, splenomegaly, jaundice and gallstones. One of the main reasons for referring these patients to the operating room is splenectomy and cholecystectomy to treat the complica...
متن کاملAnaesthetic management of a case of hereditary spherocytosis for splenectomy and cholecystectomy
Objectives:Hereditary spherocytosis is a heterogeneous group of disorder that results in the formation of abnormal red blood cells with fragile cell walls causing anaemia, jaundice, splenomegaly and ultimately gall stone formation. Most children have mild disease do not require splenectomy. Splenectomy is reserved for those with severe disease or who develop symptomatic gall stone. Individuals ...
متن کاملGrowth Failure in Hereditary Spherocytosis and the Effect of Splenectomy.
OBJECTIVE To analyze growth-failure and improvement, if any, following splenectomy in children with hereditary spherocytosis. METHODS Data collection from case-records (n=82) over 27-years (1985-2011). RESULTS Prevalence of stunting was 26%; 32% were underweight. Stunted children were older in age (P=0.006) and presented late (P=0.003). Splenectomy (n=26) improved anemia (P<0.001). However,...
متن کاملHereditary spherocytosis in children: profile and post-splenectomy outcome.
OBJECTIVE To describe profile of 82 children with hereditary spherocytosis diagnosed over a period of 27 years (1985-2011) from a single center. METHODS Retrospective analyses of case records. RESULTS The mean (SD) age at diagnosis was 6.7 (2.8) years; 7 (8.5%) were diagnosed in infancy. Pallor (100%), icterus (67%), undocumented fever (28%), splenomegaly (96%) and hepatomegaly (73%) were t...
متن کاملRed cell life span after splenectomy in hereditary spherocytosis.
Despite the persistence of spherocytosis after splenectomy in hereditary spherocytosis, it has usually been assumed that red cell life span returns completely to normal after this treatment. Diisopropyl fluorophosphate. DF(32)P, a noneluting red cell label, was given intravenously to 11 patients in five unrelated families 2-27 yr after splenectomy for typical hereditary spherocytosis. Hemoglobi...
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ژورنال
عنوان ژورنال: The journal of the Japanese Practical Surgeon Society
سال: 1994
ISSN: 0386-9776
DOI: 10.3919/ringe1963.55.1713